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Majocchi's disease

Majocchi's disease
Purpura annularis telangiectodes

Majocchi's disease, also known as Purpura annularis telangiectodes of Majocchi[1] is a not-well-recognized and uncommon skin condition characterized by purple/bluish-red 1- to 3-cm annular patches composed of dark red telangiectases with petechiae. It is one of a group of disorders referred to as pigmented purpuric dermatosis that all occur as a result of vascular inflammation and pigment deposition.[2]: 829 

Signs and symptoms

Majocchi's disease is characterized by punctuate reddish-brown macules and symmetrical, annular patches, with a tendency toward the lower extremities.[3]

Treatment

Majocchi's disease is a chronic condition for which there is no cure. It often follows a recurrent course of alternating improvement and flares. There are treatments available to help improve the symptoms for some individuals, but responses vary. Some of these treatments include the application of topical steroids and ultraviolet therapy. The use of narrowband UVB and psoralen have shown to be effective treatments for some patients with pigmented purpuric dermatoses.[3]

References

  1. ^ Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 1-4160-2999-0.
  2. ^ James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. ISBN 0-7216-2921-0.
  3. ^ a b Dhali, Tapan Kumar; Chahar, Monica; Haroon, Mohammad Asad (2015). "Phototherapy as an effective treatment for Majocchi's disease - Case report". Anais Brasileiros de Dermatologia. 90 (1): 96–99. doi:10.1590/abd1806-4841.20153067. ISSN 0365-0596. PMC 4323703. PMID 25672304.